Autoimmune/Rheumatic

Polymyositis and Dermatomyositis Overview

Polymyositis and dermatomyositis are two closely related inflammatory muscle diseases (myopathies) in which muscle fiber inflammation leads to progressive muscle weakness. While polymyositis lacks skin involvement, dermatomyositis is distinguished by its characteristic skin rash. Both are autoimmune conditions that can also affect the lungs, heart, and joints.

7

Symptoms

2

Causes

5

Treatments

1

Prevention

Condition Overview

Understand key symptoms, causes, diagnosis options, and treatment pathways for Polymyositis and Dermatomyositis Overview. This overview is intended for patient awareness and should be followed by specialist consultation.

AutoimmuneRheumaticPrevalence Available

Need Help?

Our specialists can guide you through symptoms and treatment options.

Book Appointment

24/7 Emergency: +91 1800-MEDICARE

Symptoms

  • Progressive proximal muscle weakness
  • Difficulty rising from a chair, climbing stairs, lifting arms overhead
  • Skin rash (in dermatomyositis)
  • Difficulty swallowing
  • Shortness of breath
  • Joint pain
  • Fatigue

Causes

  • Autoimmune attack on muscle tissue
  • Possible triggers: infections, malignancy, medications

Diagnosis

  • CK enzyme levels
  • Myositis-specific antibodies
  • EMG
  • MRI of muscles
  • Muscle biopsy

Treatment

  • Corticosteroids
  • Immunosuppressants (methotrexate, azathioprine)
  • IVIG
  • Rituximab
  • Physical therapy

Risk Factors

  • Female sex
  • Age 40–60
  • Association with cancer (adult DM)

Prevention

  • No known prevention

Prevalence

Combined incidence of approximately 5–10 cases per million per year.